Median cleft face syndrome.

A 7-year-old male child with normal neuro and mental development presented with facial malformations. He had hypertelorism, exotropia, broad nasal root, midline clefting of the nose and an operated scar for frontal encephalocele (Fig. 1). The anterior nares were short and narrow. His visual acuity was 6/24 in both eyes and he had bilateral optic nerve atrophy. The rest of the systems were normal. A CT scan of the head revealed normal brain structure with the presence of a bone graft in the frontal region that was grafted for frontal encephalocele (Fig. 2).